Adaptive Behavior in School-Age Children with Neurofibromatosis Type 1: Relations to Cognitive and Executive Functioning
Mentor 1
Bonnie Klein-Tasman
Location
Union Wisconsin Room
Start Date
5-4-2019 1:30 PM
End Date
5-4-2019 3:30 PM
Description
Neurofibromatosis type 1 (NF1) is an autosomal dominant genetic disorder affecting 1 in 3,000 people and is characterized by attention and learning problems. There has been minimal research regarding adaptive behavior in school-age children with NF1, and close to none examining the associations of adaptive behavior with cognitive and executive functioning. The current study will investigate adaptive behavior in school-age children, measured by the Scales of Independent Behavior (SIB-R). Additionally, this study will examine the relations between adaptive behavior and cognitive functioning, using the Differential Ability Scales (DAS-II), and executive functioning, using the Behavior Rating Inventory of Executive Functioning (BRIEF). Participants are thirty-nine (n=39) school-age children with NF1 (ages 9-13) and their parents. As part of the neuropsychological battery, the DAS-II was administered to each participant and parents completed the SIB-R and BRIEF. We expect to find that school-age children with NF1 have difficulties in adaptive behavior in comparison to other children their age, based on comparisons to normative data, along with difficulties in cognitive and executive functioning. We also expect to see significant relations of the SIB-R with the DAS-II and BRIEF, as similar associations have been noted in past research. We also anticipate specific limitations in motor skills for school age children with NF1, as difficulties in this area have been found in a past study involving preschool children with NF1. Studies regarding adaptive behavior have the potential to help inform parents and teachers about the care of children with NF1 and represents a topic that needs to be more broadly explored to more effectively prepare children with NF1 to succeed in the home at and school.
Adaptive Behavior in School-Age Children with Neurofibromatosis Type 1: Relations to Cognitive and Executive Functioning
Union Wisconsin Room
Neurofibromatosis type 1 (NF1) is an autosomal dominant genetic disorder affecting 1 in 3,000 people and is characterized by attention and learning problems. There has been minimal research regarding adaptive behavior in school-age children with NF1, and close to none examining the associations of adaptive behavior with cognitive and executive functioning. The current study will investigate adaptive behavior in school-age children, measured by the Scales of Independent Behavior (SIB-R). Additionally, this study will examine the relations between adaptive behavior and cognitive functioning, using the Differential Ability Scales (DAS-II), and executive functioning, using the Behavior Rating Inventory of Executive Functioning (BRIEF). Participants are thirty-nine (n=39) school-age children with NF1 (ages 9-13) and their parents. As part of the neuropsychological battery, the DAS-II was administered to each participant and parents completed the SIB-R and BRIEF. We expect to find that school-age children with NF1 have difficulties in adaptive behavior in comparison to other children their age, based on comparisons to normative data, along with difficulties in cognitive and executive functioning. We also expect to see significant relations of the SIB-R with the DAS-II and BRIEF, as similar associations have been noted in past research. We also anticipate specific limitations in motor skills for school age children with NF1, as difficulties in this area have been found in a past study involving preschool children with NF1. Studies regarding adaptive behavior have the potential to help inform parents and teachers about the care of children with NF1 and represents a topic that needs to be more broadly explored to more effectively prepare children with NF1 to succeed in the home at and school.
